Serveur d'exploration sur le lymphœdème

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Lymphoscintigraphic evaluation of congenital lymphedema of the newborn

Identifieur interne : 009886 ( Main/Exploration ); précédent : 009885; suivant : 009887

Lymphoscintigraphic evaluation of congenital lymphedema of the newborn

Auteurs : Carlo Bellini [Italie] ; Cesare Arioni [Italie] ; Massimo Mazzella [Italie] ; Corradino Campisi [Italie] ; Gioconda Taddei [Italie] ; Francesco Boccardo [Italie] ; Giovanni Serra [Italie]

Source :

RBID : Pascal:02-0334317

Descripteurs français

English descriptors

Abstract

The authors present a case of the Hennekam syndrome diagnosed in a newborn. Lymphedema is usually present in this syndrome, and the lymphoscintigraphic imaging findings for its detection are discussed. This case confirms the utility of lymphoscintigraphy in providing important physiologic and anatomic information for presurgical planning. An etiologic diagnosis could possibly be obtained. The procedure is relatively easy to perform, safe, reliable, minimally invasive, and not uncomfortable for the patient. It should be considered a valuable diagnostic tool, especially in newborns, in whom conventional contrast lymphoangiography is difficult to perform.


Affiliations:


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Le document en format XML

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<term>Congenital</term>
<term>Diagnosis</term>
<term>Female</term>
<term>Humans</term>
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<term>Déficience intellectuelle</term>
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<term>Lymphoscintigraphie</term>
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<term>Malformations multiples (génétique)</term>
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<term>Nouveau-né</term>
<term>Radiopharmaceutiques</term>
<term>Soins préopératoires</term>
<term>Sulfocolloïde de technétium (99mTc)</term>
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<term>Female</term>
<term>Humans</term>
<term>Infant, Newborn</term>
<term>Intellectual Disability</term>
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<term>Déficience intellectuelle</term>
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<div type="abstract" xml:lang="en">The authors present a case of the Hennekam syndrome diagnosed in a newborn. Lymphedema is usually present in this syndrome, and the lymphoscintigraphic imaging findings for its detection are discussed. This case confirms the utility of lymphoscintigraphy in providing important physiologic and anatomic information for presurgical planning. An etiologic diagnosis could possibly be obtained. The procedure is relatively easy to perform, safe, reliable, minimally invasive, and not uncomfortable for the patient. It should be considered a valuable diagnostic tool, especially in newborns, in whom conventional contrast lymphoangiography is difficult to perform.</div>
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